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KMID : 0361120130270010024
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Korean Journal of Transplantation
2013 Volume.27 No. 1 p.24 ~ p.28
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A Case of Rapidly Progressive Primary Sclerosing Cholangitis Requiring Liver Transplantation
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Lim Tae-Seop
Park Jun-Yong
Kim Soon-Il
Kang Huap-Yong
Chung Moon-Jae
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Abstract
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Primary sclerosing cholangitis (PSC) is a slowly progressive cholestatic liver disease. In cases of PSC, liver transplantation is the only effective treatment that can delay the disease`s natural course. We report a case of rapidly progressive PSC requiring liver transplantation. A 52-year-old woman visited our hospital with abdominal pain. There was no evidence of PSC, as there was no elevation in cholestatic liver enzymes at her first visit. Although her total bilirubin was in a normal range at the initial visit, liver dysfunction progressed rapidly. Despite endoscopic procedures and ursodeoxycholic acid intake, total bilirubin levels rose to 18.9 mg/dL, and liver transplantation was performed 17 months after her first visit. PSC was pathologically confirmed after liver transplantation.
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KEYWORD
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Primary sclerosing cholangitis, Liver transplantation, Ursodeoxycholic acid, Endoscopic retrograde cholangiopancreatography, Magnetic resonance cholangiopancreatography
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